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Таким образом, имелись медицинские показания для двустороннего удлинения ног. Из соображений пропорциональности, чтобы новая длина ног гармонировала с туловищем и руками, пациентка выбрала увеличение роста на 12 см.",[],[337],"lg:col-span-6",{"_uid":339,"image":340,"title":343,"component":344,"copyright":9,"image_style":345,"component_style":346},"681b5e04-476c-4569-bb0a-6e5d6fa49476",{"id":341,"alt":101,"name":9,"focus":101,"title":101,"filename":342,"copyright":101,"fieldtype":11},1773613,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F1908x3814\u002Ff471779373\u002Fcase7_7.jpg","Непропорциональная низкорослость при ахондроплазии","Image",[],[347],"col-span-3",{"_uid":349,"image":350,"title":353,"component":344,"copyright":9,"image_style":354,"component_style":355},"3bb80328-fb66-4beb-a733-4e2ba385100e",{"id":351,"alt":101,"name":9,"focus":101,"title":101,"filename":352,"copyright":101,"fieldtype":11},1773145,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F639x1279\u002F85b9395344\u002Fcase7_2.jpg","Короткие бедра и голени и деформированные суставы",[],[347],{"_uid":357,"text":358,"component":324,"text_style":359,"component_style":360},"eb1da6c7-dc84-492b-abdb-78b765d5dfe3","## Лечение",[],[],{"_uid":362,"text":363,"style":364,"component":365,"component_style":366},"e3ef6667-9133-4281-9246-598b915c5656","Расходы на двустороннее удлинение ног были покрыты государственным медицинским страхованием, поскольку при низкорослости, обусловленной заболеванием, имеются медицинские показания.","green","Info",[],{"_uid":368,"text":369,"component":324,"text_style":370,"component_style":371},"cb816814-a9dc-4843-ad55-482184380a72","Для того чтобы сохранить независимую мобильность на протяжении всего лечения, ноги удлинялись поочередно. На первом этапе левая нога была удлинена с помощью двух дистракционных интрамедуллярных гвоздей FITBONE - по одному в левом бедре и в левой голени. Временная разница в длине ноги была легко компенсирована ортопедической подкладкой в обуви. После достаточного образования новой костной ткани в левой ноге, через 7 месяцев такая же процедура была проведена на правой ноге. Регулярные самостоятельные упражнения и ночное положение в пластиковой шине во время удлинения улучшили подвижность и предотвратили контрактуры коленного сустава.",[],[337],{"_uid":373,"image":374,"title":377,"component":344,"copyright":9,"image_style":378,"component_style":379},"fd67caef-6c85-477c-9540-f71c37a07f94",{"id":375,"alt":101,"name":9,"focus":101,"title":101,"filename":376,"copyright":101,"fieldtype":11},1773148,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F1626x3251\u002Fc10238d541\u002Fcase7_5.jpg","Завершение удлинения левой ноги",[],[347],{"_uid":381,"image":382,"title":385,"component":344,"copyright":9,"image_style":386,"component_style":387},"95708aa4-f73b-47d6-8c6d-120455f7ed81",{"id":383,"alt":101,"name":9,"focus":101,"title":101,"filename":384,"copyright":101,"fieldtype":11},1773150,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F765x1528\u002F58d8f54dda\u002Fcase7_6.jpg","Дистракционные интрамедуллярные гвозди в левом бедре и левой голени",[],[347],{"_uid":389,"text":390,"component":324,"text_style":391,"component_style":392},"170dac99-73f7-4789-92ed-dba484f98509","## Результат",[],[],{"_uid":394,"text":395,"component":324,"text_style":396,"component_style":397},"17533fa5-6970-4112-8a33-becf612b70af","После завершения лечения с удлинением на 12 см обе ноги были одинаковой длины и прямыми, диапазон движения суставов был в пределах нормы с обеих сторон. Рост пациентки теперь составлял 140 см, и в слегка приподнятой обуви она могла прекрасно справляться с повседневной жизнью без каких-либо ограничений.",[],[337],{"_uid":399,"image":400,"title":403,"component":344,"copyright":9,"image_style":404,"component_style":405},"b0f7875b-88f8-4363-8294-6e5ed53cf2aa",{"id":401,"alt":101,"name":9,"focus":101,"title":101,"filename":402,"copyright":101,"fieldtype":11},1773614,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F1511x3022\u002F1d525f798f\u002Fcase7_8.jpg","Гармоничные пропорции после удлинения ног с обеих сторон",[],[347],{"_uid":407,"image":408,"title":411,"component":344,"copyright":9,"image_style":412,"component_style":413},"f4a58ff5-f138-46a2-bddb-11c4261ddbac",{"id":409,"alt":101,"name":9,"focus":101,"title":101,"filename":410,"copyright":101,"fieldtype":11},1773146,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F748x1498\u002F00f9c3c59f\u002Fcase7_4.jpg","Прямые ноги одинаковой длины после удлинения на 12 см",[],[347],{"_uid":415,"title":416,"stories":417,"component":450},"b0322016-634a-4d3f-b56a-f323cbdf48e7","Дополнительная информация",[418,426,434,442],{"uuid":419,"full_slug":420,"content":421},"e57bb07e-1328-4c0d-859c-9d550494b005","ru\u002Ftematicheskie-issledovaniya\u002Fipokhondroplaziya",{"_uid":319,"_editable":-1,"image":422,"intro":425,"meta_title":285},{"id":423,"alt":101,"name":9,"focus":101,"title":101,"filename":424,"copyright":101,"fieldtype":11},1773170,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F714x1427\u002F15294dd855\u002Fcase_8_1.jpg","У 14-летней пациентки имелась непропорциональная низкорослость с исходным ростом 132 см как следствие генетически подтвержденной гипохондроплазии.",{"uuid":427,"full_slug":428,"content":429},"bbe30671-7d75-4887-ae69-7486b7ec05a3","ru\u002Ftematicheskie-issledovaniya\u002Fvrozhdennoe-ukorochenie-nog-2",{"_uid":319,"_editable":-1,"image":430,"intro":433,"meta_title":261},{"id":431,"alt":101,"name":9,"focus":101,"title":101,"filename":432,"copyright":101,"fieldtype":11},1773078,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F1842x3682\u002F1b72f797e4\u002Fcase2_1.jpg","У 16-летней пациентки было врожденное укорочение на 5,5 см после завершения роста, затрагивающее как бедро, так и голень.",{"uuid":435,"full_slug":436,"content":437},"c54e7280-5fd9-4983-9d2b-1f361a29926c","ru\u002Ftematicheskie-issledovaniya\u002Fukorochenie-nogi-posle-travmy",{"_uid":319,"_editable":-1,"image":438,"intro":441,"meta_title":270},{"id":439,"alt":101,"name":9,"focus":101,"title":101,"filename":440,"copyright":101,"fieldtype":11},1773098,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F910x1820\u002F57441f619f\u002Fcase3_5.jpg","26-летний пациент получил открытый перелом голени в результате аварии на мотоцикле.",{"uuid":443,"full_slug":444,"content":445},"10639b74-dbd9-4f3e-ba7b-f33f65aa4ee9","ru\u002Ftematicheskie-issledovaniya\u002Fukorochenie-nogi-v-rezultate-neschastnogo-sluchaya-2",{"_uid":319,"_editable":-1,"image":446,"intro":449,"meta_title":273},{"id":447,"alt":101,"name":9,"focus":101,"title":101,"filename":448,"copyright":101,"fieldtype":11},1773088,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F1818x3634\u002F9886998230\u002Fcase4_1.jpg","27-летняя пациентка перенесла перелом бедренной кости в возрасте 12 лет.","Reference",{"id":452,"alt":101,"name":9,"focus":101,"title":101,"filename":453,"copyright":101,"fieldtype":11},1773147,"https:\u002F\u002Fa.storyblok.com\u002Ff\u002F56859\u002F2000x4000\u002F94580a5a5b\u002Fcase7_1.jpg","У 14-летней пациентки на фоне генетически подтвержденной ахондроплазии имелась непропорциональная низкорослость с исходным ростом 128 см.","Page",[],[],"У 14-летней пациентки с ахондроплазией имелась непропорциональная низкорослость (рост 128 см). Удлинение ног изменило ее жизнь.","achondroplasie","ru\u002Ftematicheskie-issledovaniya\u002Fakhondroplaziya",100,[],5185868,"ceef2a7a-209c-4a7c-9e67-f6623f822846","2020-12-29T13:15:35.000Z",[],"fallbeispiele\u002Fachondroplasie",[469,473,477,481,483],{"path":470,"name":471,"lang":472,"published":21},"cases\u002Fachondroplasia","Achondroplasia","en",{"path":474,"name":475,"lang":476,"published":21},"estudios-de-caso\u002Facondroplasia","Acondroplasia","es",{"path":478,"name":479,"lang":480,"published":21},"drasat-alhalh\u002Faltqzm","التقزم","ar",{"path":482,"name":282,"lang":203,"published":21},"tematicheskie-issledovaniya\u002Fakhondroplaziya",{"path":484,"name":485,"lang":486,"published":21},"an4-li4-yan2-jiu1\u002Fzhu1-ru2-zheng4","侏儒症","zh",1793682390335]